Modified facelift in severe plexiform neurofibromatosis associated with venous vascular malformation: Case report.

Annales de chirurgie plastique et esthetique 2023 Vol.68(2) p. 173-179

Mayer HF, Palacios Huatuco RM, Petersen ML, Garcia Rodriguez B, Peralta OA

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Abstract

Neurofibromatosis is an autosomal dominant disorder characterized by tumors of the nervous system and skin. Plexiform neurofibromas are common complications of neurofibromatosis type 1 and can cause large facial deformities. Vascular anomalies are in turn a rare manifestation of neurofibromatosis. We present the case of a 48-year-old female patient with right hemifacial neurofibromatosis associated with venous vascular malformation, previously treated surgically and then with sclerosing agents, determining severe residual facial deformity. Her surgical approach using a modified facelift technique associated with partial tumor debulking and lipofilling seems to be a valid technical alternative for these highly complex cases that require a customized approach after exhaustive preoperative evaluation.

추출된 의학 개체 (NER)

유형영어 표현한국어 / 풀이UMLS CUI출처등장
시술 facelift 안면거상술 dict 2
해부 plexiform scispacy 1
해부 skin scispacy 1
해부 lipofilling scispacy 1
합병증 facial scispacy 1
질환 plexiform neurofibromatosis scispacy 1
질환 venous vascular malformation C0158570
Vascular anomaly
scispacy 1
질환 Neurofibromatosis C0085113
NF1 gene
scispacy 1
질환 autosomal dominant disorder C3899989
Autosomal Dominant Disorder
scispacy 1
질환 tumors C0027651
Neoplasms
scispacy 1
질환 Plexiform neurofibromas C0206728
Plexiform Neurofibroma
scispacy 1
질환 Vascular anomalies C0158570
Vascular anomaly
scispacy 1
질환 right hemifacial neurofibromatosis scispacy 1
질환 sclerosing scispacy 1
질환 tumor C0027651
Neoplasms
scispacy 1
질환 Case scispacy 1
기타 venous vascular scispacy 1
기타 Vascular scispacy 1
기타 patient scispacy 1

MeSH Terms

Humans; Female; Middle Aged; Rhytidoplasty; Neurofibromatosis 1; Neurofibroma, Plexiform; Vascular Malformations; Preoperative Care

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