Harlequin Ichthyosis: A Surgical Perspective.

Pediatric dermatology 2016 Vol.33(5) p. e327-32

Pet MA, Gupta D, Tse RW

관련 도메인

Abstract

Limb constriction or encasement in patients with harlequin ichthyosis can cause tissue injury resulting in necrosis and auto-amputation. Surgical release of constrictive plaques has been previously demonstrated, but the perioperative and intraoperative considerations surrounding this infrequent intervention have not been discussed in detail. This report documents a case of harlequin ichthyosis requiring surgical treatment, focusing on the importance of early surgical consultation, risks of surgery, indications for and timing of surgical intervention, and the details of the operation.

추출된 의학 개체 (NER)

유형영어 표현한국어 / 풀이UMLS CUI출처등장
해부 Limb scispacy 1
해부 tissue scispacy 1
합병증 necrosis 괴사 dict 1
질환 Ichthyosis C0020757
Ichthyoses
scispacy 1
질환 harlequin ichthyosis C0239849
Harlequin Fetus
scispacy 1
기타 patients scispacy 1

MeSH Terms

Acitretin; Administration, Oral; Compartment Syndromes; Decompression, Surgical; Dermatologic Surgical Procedures; Female; Follow-Up Studies; Humans; Ichthyosis, Lamellar; Infant, Newborn; Rare Diseases; Risk Assessment; Severity of Illness Index; Surgery, Plastic; Treatment Outcome

🔗 함께 등장하는 도메인

이 논문이 속한 카테고리와 같은 논문에서 자주 함께 다뤄지는 카테고리들

관련 논문