True hermaphroditism presenting as bilateral gynecomastia in an adolescent phenotypic male.

[OBJECTIVE] To report a rare case of true hermaphroditism presenting in adolescence as bilateral gynecomastia in a phenotypic male.

[DESIGN] Case report.

[SETTING] Academic medical center.

[PATIENT(S)] A 19-year-old phenotypic male who presented with pronounced bilateral gynecomastia and was ultimately diagnosed with true hermaphroditism.

[INTERVENTION(S)] Endoscopic removal of the internal female genital tract (hemiuterus and ovary), reduction mammoplasty, repair of penile chordee, and left testicular prosthesis placement.

[MAIN OUTCOME MEASURE(S)] Diagnosis and treatment of true hermaphroditism.

[RESULT(S)] Bilateral mammoplasties, repair of a penile chordee, placement of a left testicular prosthesis, and excision of the left hemiuterus and ovary resulted in return to testicular function in this true hermaphrodite.

[CONCLUSION(S)] Although rare, true hermaphroditism should be suspected in male patients presenting with bilateral breast enlargement in adolescence.