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Aplasia cutis congenita. A follow-up evaluation after 25 years.

Archives of dermatology 1981 Vol.117(4) p. 232-3

Munkvad JM, Nielsen AO, Asmussen T

📝 환자 설명용 한 줄

【연구 목적】 선천성 무피증(aplasia cutis congenita)은 보고된 사례가 300건 미만인 희귀 질환으로, 본 연구는 광범위한 피부 병변을 가진 환자에서 25년간의 장기 추적 관찰을 통해 질환의 자연 경과와 심리적 영향, 그리고 수술적 중재의 효과를 평가하는 것을 목적으로 한다.

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BibTeX ↓ RIS ↓
APA Munkvad JM, Nielsen AO, Asmussen T (1981). Aplasia cutis congenita. A follow-up evaluation after 25 years.. Archives of dermatology, 117(4), 232-3. https://doi.org/10.1001/archderm.117.4.232
MLA Munkvad JM, et al.. "Aplasia cutis congenita. A follow-up evaluation after 25 years.." Archives of dermatology, vol. 117, no. 4, 1981, pp. 232-3.
PMID 7212745

Abstract

Aplasia cutis congenita is a rare disease with less than 300 cases reported in the literature. A patient with extensive involvement of the skin was observed for 25 years. During adolescence, a reactive depression related to the residual cicatricial alopecia on the left side of the scalp developed. The psychiatric distress disappeared after corrective surgery was performed. It is recommended that patients with this disorder be regularly observed to select cases appropriate for early plastic surgery.

추출된 의학 개체 (NER)

유형영어 표현한국어 / 풀이UMLS CUI출처등장
해부 skin scispacy 1
해부 cicatricial scispacy 1
해부 left scispacy 1
해부 scalp scispacy 1
질환 Aplasia cutis congenita C0282160
Aplasia Cutis Congenita
scispacy 1
질환 depression C0011570
Mental Depression
scispacy 1
질환 alopecia C0002170
Alopecia
scispacy 1
질환 psychiatric C0033873
Psychiatry Specialty
scispacy 1

MeSH Terms

Adjustment Disorders; Adult; Alopecia; Dermatologic Surgical Procedures; Female; Follow-Up Studies; Humans; Skin Abnormalities; Surgery, Plastic