Ten years experience with masculinizing genitoplasty in male pseudohermaphroditism due to 17 beta-hydroxysteroid dehydrogenase deficiency.
【연구 목적】 17베타-하이드록시스테로이드 탈수소효소 결핍증으로 인한 남성 의사간성증 환자에서 남성화 성형수술(masculinizing genitoplasty)의 장기적 임상 결과를 평가하고, 수술 시기와 방식이 미용 및 기능적 결과에 미치는 영향을 규명하는 것이 본 연구의 목적이다.
APA
Farkas A, Rosler A (1993). Ten years experience with masculinizing genitoplasty in male pseudohermaphroditism due to 17 beta-hydroxysteroid dehydrogenase deficiency.. European journal of pediatrics, 152 Suppl 2, S88-90. https://doi.org/10.1007/BF02125448
MLA
Farkas A, et al.. "Ten years experience with masculinizing genitoplasty in male pseudohermaphroditism due to 17 beta-hydroxysteroid dehydrogenase deficiency.." European journal of pediatrics, vol. 152 Suppl 2, 1993, pp. S88-90.
PMID
8393406
Abstract
An extensive survey in a highly inbred Arab community documented over 60 cases of male pseudohermaphroditism due to 17 beta hydroxysteroid dehydrogenase deficiency. During a period of 10 years (1981-1991), 16 such patients underwent masculinating genitoplasty. Two children have had a one stage corrective genitoplasty while all others (2 adults, 3 adolescents and 9 children) had staged operations. Cosmetic and functional results are very encouraging in children and adolescents but very poor among adults. Based on our experience and follow-up, we advocate early sex assignment and early masculinizing genitoplasty with preoperative hormonal therapy to male pseudohermaphrodites due to 17 beta hydroxysteroid dehydrogenase deficiency.
추출된 의학 개체 (NER)
| 유형 | 영어 표현 | 한국어 / 풀이 | UMLS CUI | 출처 | 등장 |
|---|---|---|---|---|---|
| 해부 | genitoplasty
|
scispacy | 1 | ||
| 합병증 | genitoplasty
|
scispacy | 1 | ||
| 질환 | masculinizing genitoplasty
|
scispacy | 1 | ||
| 질환 | beta-hydroxysteroid dehydrogenase deficiency
|
C0342471
3 beta-Hydroxysteroid dehydrogenase deficiency
|
scispacy | 1 | |
| 질환 | masculinating genitoplasty
|
scispacy | 1 | ||
| 질환 | genitoplasty
|
scispacy | 1 | ||
| 기타 | beta-hydroxysteroid dehydrogenase
|
scispacy | 1 | ||
| 기타 | children
|
scispacy | 1 |
MeSH Terms
17-Hydroxysteroid Dehydrogenases; Adolescent; Adult; Child, Preschool; Combined Modality Therapy; Disorders of Sex Development; Follow-Up Studies; Humans; Infant; Male; Reoperation; Surgery, Plastic; Surgical Procedures, Operative; Testosterone